Associated Clinical Conditions
P316: SUBMANDIBULAR SIALOLITHIASIS IN A PATIENT WITH CYSTIC FIBROSIS
I. Adams(1), D. Rostalski(2), V. Sollich(1)
(1) Department of General Paediatrics and Neonatology, MedicalFaculty, Otto von Guericke University, (2) Department of Otorhinolarynology,Medical Faculty, Otto von Guericke University, Magdeburg, GermanyP304: URIC ACID METABOLISM IN CYSTIC FIBROSIS
M.Fotoulaki(1), A Makedou(2), S Nousia-Arvanitakis(1)
(1) Fourth Department of Pediatrics,Aristotle University, (2) Biochemical Laboratory,Fourth Department of Pediatrics GreeceP314: PSEUDO-BARTTER'S SYNDROME: A SPECTRUM OF DISORDERS ASSOCIATED WITH CYSTIC FIBROSIS
V. Hresic-Krsulovic, M. Percl, I. Golmajer-Vlahovic, J. Cepin-Bogovic
Children's Hospital Zagreb, Klaiceva 16 , University of Zagreb, Medical School, Department of Pediatrics, CroatiaP317: FAVOURABLE OUTCOME OF MULTIPLE CEREBRAL ABSCESSES IN A CYSTIC FIBROSIS PATIENT
M.A. Monti(1), G. Pizzamiglio(1), N. Gervasini(1), A. Giunta(2), G.C. Secchi(1)
(1) Centro Fibrosi Cistica Regione Lombardia - Sezioni Adulti -I.C.P - Milano, (2) Centro Fibrosi Cistica Regione Lombardia, ItalyP267: HYPERCALCIURIA IN CYSTIC FIBROSIS
S Nousia-Arvanitakis(1), M Fotoulaki(1), A Makedou(2)
(1) Fourth Department of Pediatrics,Aristotle University, (2) Biochemical Laboratory,Fourth Department of Pediatrics, GreeceP315: PSEUDO BARTTER-SYNDROME IN TURKISH CYSTIC FIBROSIS CHILDREN
Ebru Yalcin(1), Ilker Cetin(1), Mustafa Koyun(1), Deniz Dogru(2), Nural Kiper(3), Ugur Ozcelik(4), Ayhan Gocmen(3)
(1) Pediatrician, (2) Assistant Professor of Pediatrics, (3) Professor of Pediatrics, (4) Associate Professor of Pediatrics,Ankara, Turkey
P355: INFECTION CONTROL POLICIES IN A CYSTIC FIBROSIS CENTRE - WHAT DO PATIENTS WANT TO DO?
A Bowling , M Dodd , J Milnes , K Webb , A Jones
Adult CF Centre, South Manchester University Hospitals NHS Trust, Manchester, UKP151: SIMULATION OF A LONG-DISTANCE FLIGHT IN PATIENTS WITH CYSTIC FIBROSIS
K. Brueckner, R. Fischer, S. Meyer, R. M. Huber
Pneumology, Medizinische Klinik Innenstadt, Ludwig-Maximilians-University, Munich. GermanyP359: A REVIEW OF THE HOMECARE SERVICE OFFERED BY A PAEDIATRIC CYSTIC FIBROSIS CLINIC
J Burton
Great Ormond Street Hospital for Children NHS Trust, London, UKP159: TELEMETRIC MONITORING SYSTEM (TMS) FOR DOMICILE NON INVASIVE MECHANICAL VENTILATION (DNIMV) IN END STAGE CYSTIC FIBROSIS (CF) PATIENTS WAITING FOR DOUBLE LUNG TRANSPLANTATION (DLT)
G.Cimino, S.Bertasi, F.Alatri, L.Graziano, S.Cingolani, S.Quattrucci
Pediatrics Department Policlinico Umberto I University of RomeLa Sapienza , Rome, ItalyP326: CYSTIC FIBROSIS - WHO CARES ?
K. Deem (1), F. Thornhill (1), A. Dewar (1)
Paediatric Department, Poole Hospital NHS Trust UKP321: MEDICAL AND SOCIAL PROVISION OF CYSTIC FIBROSIS PATIENTS
A.Kapranov, Z.Biistinova, I.Osipova, A.Voronkova , N.Kapranov, N.Kashirskaya
Research Centre for Medical Genetics RAMS, Moscow, Russia
P323: WEIGHT GAIN AND RESPIRATORY FUNCTION IN RELATION TO SCHOOL HOLIDAYS FOR CHILDREN WITH CYSTIC FIBROSIS
Alan Cade , Maggie O'Connell, Steven P Conway, Keith G Brownlee
Regional paediatric cystic fibrosis unit, St. James' University hospital, Beckett Street, Leeds LS9 7TF. UKP268: BONE MINERAL AND BODY COMPOSITION IN CHILDREN WITH CYSTIC FIBROSIS
S Conway (1), B Oldroyd (2), K Brownlee (1), S Wolfe (1), S Evans (1) J Truscott (2)
(1)Regional Paediatric Cystic Fibrosis Unit, St James's University Hospital, Leeds UK., (2) Centre for Bone and Body Composition Research, The General Infirmary, Leeds, UKP269: BONE TURNOVER IN CHILDREN WITH CYSTIC FIBROSIS
S Conway (1), B Oldroyd (2), K Brownlee (1), S Wolfe(1), S Evans (1), W Fraser (3), J Truscott (2)
(1) Regional Paediatric Cystic Fibrosis Unit, St James's University Hospital, Leeds UK, (2) Centre for Bone and Body Composition Research, Leeds General Infirmary, Leeds UK, (3) Department of Clinical Chemistry, University of Liverpool, Liverpool UKP153: IS POOR OUTCOME PREDICTABLE IN EARLY MANIFESTATIONS OF CYSTIC FIBROSIS IN YOUNG CHILDREN?
L Dracea (1), O. Falup-Pecurariu (1), S. Buzinschi (1), S. Rogoz (1), G. Benga (2), M. Schwarz (3), I. Popa (4)
(1) Children's Hospital/ University Hospital of Brasov, Romania, (2) Genetic Department, University Hospital Cluj-Napoca,Romania, (3) Genetic Department, Royal Manchester Children's Hospital,UK, (4) IInd Pediatric Clinic, National CF Center Timisoara, RomaniaP265: STATUS OF BONE MINERAL CONTENT IN A GROUP OF CHILDREN WITH CYSTIC FIBROSIS
Lowdon J, Nathan M, Doull IJM.
Paediatric CF/Respiratory unit, Department of Child Health, University Hospital of Wales, Cardiff, Wales.P274: MALE CF BODY BUILDERS AND EFFECTS OF THE USE OF MUSCLE ENHANCING SUBSTANCES.
S Pandya , M Ledson , M Walshaw
Regional Adult CF Unit , Liverpool, UKP154: FACTORS INFLUENCING THE COURSE OF CF IN CZECH PATIENTS.
D. Zemkova (1), M. Hladmkova (2), J. Bartosova (1), A. Zapletal (1), M. Macek Jr. (3), V. Vavrova (1)
(1) 2nd Paediatric Department, Charles University 2nd Medical School and University Hospital Motol, (2) Institute of Medical Informatics, Charles University 2nd Medical School, (3) Institute of Biology & Medical Genetics, Charles University 2nd Medical SchoolS12.3: ATYPICAL CF AND THE CLINICAL CONSEQUENCES
C.Wallis
Great Ormond Street Hospital for Children, London, UK
P44: IMPACT OF ADDITIONAL TOOLS ON THE DIAGNOSIS OF CYSTIC FIBROSIS
C. Barreto(1), A. Lopes(1), L. Pereira(1), J. Thomas(2), M. Mall(2), M. Amaral(3)
(1) Cystic Fibrosis Centre, Pediatric Department, University ofHospital Santa Maria, Lisbon, Portugal, (2) Universitats-Kinderklinic, Albert-Ludwigs UniversitatFreiburg, Germany, (3) Centro de Genitica Humana, Instituto Nacional de Saude,Lisbon, PortugalOP2.6: CF DIAGNOSIS: INTESTINAL CURRENT MEASUREMENTS ON RECTAL SUCTION BIOPSIES VERSUS THE SWEAT TEST.
I. Bronsveld(1), H. de Jonge(2), M. Sinaasappel(1)
(1) Department of Pediatric Gastroenterology, Sophia Children'sHospital, Rotterdam, The Netherlands, (2) Department of Biochemistry, Erasmus University, Rotterdam,The NetherlandsP357: ECHOGENIC BOWEL ON ULTRASOUND SCAN LEADING TO ANTENATAL DIAGNOSIS OF CF : THE ROLE OF THE CF TEAM
JJ Cottrell, EF Burrows, DP Heaf
Royal Liverpool Childrens Hospital, Alder Hey, Liverpool, UKP97: POSITIVE SWEAT TEST FOLLOWING MENINGOCOCCAL SEPTICAEMIA
M. Eisenhut, K. Southern
Institute of Child Health, University of Liverpool,Alder Hey Childrens Hospital, Eaton Road, Liverpool, Great Britain.P43: EMPLOYING THE NASAL POTENTIAL DIFFERENCE AS A DIAGNOSTIC TEST FOR CYSTIC FIBROSIS IN NEONATES; POTENTIAL PITFALLS
E A, Gaillard (1), N J, Shaw (1), H L , Wallace (2), N V, Subhedar (1), K W, Southern (2)
(1) Liverpool Women's Hospital, Liverpool, UK., (2) Institute of Child Health, University of Liverpool, Liverpool UKP230: THE LATE DIAGNOSIS OF CYSTIC FIBROSIS
P. Kohout(1), K. Vonkova(2)
(1) IInd Department of Internal Medicine,(2) Dept.of pneumology, Charles University Hospital, Hradec Kralove, Czech RepublicP353: THE DIAGNOSIS OF CF BEYOND INFANCY: ARE PRESENTING FEATURES MILD OR MISSED?
J, Leaver, M, Turner, T, David, L, Patel
Department of Child Health, University of Manchester and Booth Hall Childrens Hospital, Manchester, UKP310: FABRICATED ILLNESS IN CYSTIC FIBROSIS; A ROLE FOR AIRWAY ION TRANSPORT STUDIES ?
Southern KW(1), Burrows EF(2), Cottrell JJ(2), Wallace HL(1), Barker PM(3)
(1) Department of Paediatrics, University of Liverpool, UK, (2) Regional Paediatric CF Unit, Alder Hey Children's Hospital,UK, (3) University of North Carolina at Chapel Hill, North Carolina, USAOP2.5: THE USE OF NASAL POTENTIAL DIFFERENCE MEASUREMENTS IN RECURRENT PANCREATITIS
M Wilschanski (1), Y Yaakov (1), H Blau (2), H Bibi (3), N Weisman (4), R Arnon (5), A Klar (6), E Broide (7), E Kerem (1)
(1) CF Center, Shaare Zedek Medical Center, Jerusalem, (2) CF Center, Schneider Children's Hospital, Petach Tiqva, (3) Pediatric Pulmonology, Barzilai Medical Center, Ashkelon, (4) Clinical Nutrition Unit, Sorasky Medical Center, Tel Aviv, (5) Pediatric Gastroenterology, Sorasky Medical Center, Tel Aviv, (6) Dept. of Pediatrics, Bikur Cholim Hospital, Jerusalem, (7) Pediatric Gastroenterology, Assaf Harofeh Hospital, Tzriffin